#SOBANUKIRWA ECTOPIC HEART

Ectopic heart (mu Cyongereza) cyangwa ectopia cordis ni indwara idasanzwe ibaho umwana akivuka, aho umutima uba hanze y’igituza (thorax), aho kuba imbere mu gituza nk'uko bisanzwe.

Iterwa n’iki?

Iyi ndwara iterwa n’ikibazo kibaho mu gihe umwana akiri ur embryo (mu mezi atatu ya mbere y’iterambere rye), aho igice cy’igituza (sternum) kidafunga neza, bikarangira umutima usigaye hanze. Impamvu nyamukuru ntiziramenyekana neza, ariko hari aho biba bifitanye isano n’ibibazo by’imisemburo (hormones), impinduka kuri ADN, cyangwa ibindi bibazo by’iterambere ry’umubiri.

Ese iravurwa? Ivurwa gute?

Yego, iravurwa ariko biragorana cyane. Ubuvuzi bwayo akenshi buba ari u kubaga umwana kugira ngo bashyire umutima aho wagombaga kuba, barangize igice cy'igituza cyari kituzuye.

Hari uburyo bubiri bukomeye bwo kuyivura:

1. Kubaga hakiri kare – Iyo bibonetse umwana akivuka, abaganga bashobora kugerageza kumusubiza umutima mu gituza bakoresheje ibikoresho byabugenewe.

2. Kubaga by’inzego nyinshi cg mubyiciro (staged surgery) – Iyo umutima utabasha guhita usubizwa mu gituza, abaganga babanza gukora ibindi bikorwa by’ubuvuzi (nk’inkingi z’inyuma) kugira ngo bikunde.

   
   

Ese abantu benshi babaho nyuma y’iyi ndwara?

Oya, kuko ari indwara ikomeye cyane kandi igira ibyago byinshi byo kuba yatera urupfu. Abana bayivukana akenshi ntibamara igihe kinini, cyane cyane iyo batavuwe vuba. Gusa, hari bake babashije gukira kubera kubagwa neza.

Muri make: Ectopic heart ni indwara ikomeye aho umutima uba hanze y’ikiribwa. Iravurwa binyuze mu kubaga, ariko ni indwara igira ibyago byinshi byo gutera urupfu.

Ni HORMONE ZINGANA IKI ZATERA IKIBAZO CYA *ECTOPIC HEART*

Mu by’ukuri, ectopia cordis ntabwo iterwa n'uko imisemburo (hormones) yabaye mike cyangwa myinshi gusa mu buryo bumwe. Ahubwo, ikibazo kiba ku buryo imisemburo igenga iterambere ry’umwana (embryo development hormones) itakoze neza cyangwa se igatangira gukora nabi ku gihe kitari cyo.

Iyo imisemburo nko:

Progesterone,

Estrogens,

Retinoic acid (ituruka kuri vitamin A)

n’indi, iyo igabanutse cyane cyangwa ikiyongereye cyane mu gihe cy'ingenzi cyo kwiremamo kw'ibice by’umubiri (by'umwihariko mu mezi 2-3 ya mbere), bituma ibice bimwe by’umubiri bidakura neza, harimo no kuba igituza kitaziba neza.

Mu buryo burambuye:

Imisemburo mikeya ituma igice cy'igituza (sternum) kidafunga neza.

Imisemburo myinshi cyane nayo ishobora gutera imyitwarire idasanzwe y’uturemangingo (cells) twubaka igituza, bigatuma umutima usigara hanze.

Icy’ingenzi si gusa umubare wa hormones, ahubwo ni uko kubaho kw’iyo misemburo, igihe ikenerwa n'uburyo ikora neza byose bigira uruhare. Akenshi, impinduka kuri ADN (genetic mutations) nazo zituma ibi bibaho, zikajyana n’imikorere mibi y’imisemburo.

Mu magambo magufi:

- Imisemburo mikeya cyane cyangwa myinshi cyane zombi zishobora kugira uruhare mu gutuma ectopia cordis iba, ariko akenshi ikibazo gikomoka ku kuba iterambere ry'umwana ridakurikije gahunda isanzwe.

IMWE MUMISEMBURO IFASHA UMWANA (urusoro) MUGUKURA

1. Imisemburo ifite uruhare runini mu iterambere ry'umwana munda:

Progesterone

Uyu musemburo uturuka mu murerantanga (ovary) no mu ruhago rw'inda (placenta) iyo inda imaze gufatwa.

Utegurira nyababyeyi kwakira no kurinda embryo (utangira gufata ifumbire) kandi utuma imyanya y’umwana imbere mu nda ikura neza.

Ikibazo: Iyo progesterone ari nke cyane, urwego rwo gukura no gufunga neza ibice nk’igituza rwangirika.

Estrogen

Ifasha mu gukura kw’uturemangingo (cells) no gutuma inyama z’umubiri zikura neza, harimo igituza.

Ikibazo: Estrogen ikabije cyangwa nke cyane igihe kitari cyo ishobora gutuma uturemangingo tudakora gahunda neza, bigatera ibibazo nk'ectopia cordis.

Retinoic acid (ituruka kuri vitamin A)

Ni ingenzi cyane mu gutuma umubiri w'umwana ugira imiterere isanzwe (cyane cyane mu gufunga sternum).

Ikibazo: Ikabije ya vitamin A (nko gufata imiti ikungahaye cyane kuri vitamin A cyangwa supplements nyinshi) ishobora gutera ikibazo gikomeye mu gukura k'umutima n'igituza.

Thyroid hormones (T3 na T4)

Imisemburo ituruka ku ngingo yitwa thyroïde, igira uruhare mu mikurire rusange y’uturemangingo.

Ikibazo: Kuba mutwite ufite hypothyroidisme (imisemburo ya thyroid mike) bishobora gutuma umwana adakura neza, harimo n’igituza.

2. Ese babyitaho gute igihe umuntu atwite?

Isuzuma ry’imisemburo: Abagore batwite baba bakwiye gupimwa imisemburo nka progesterone, estrogens, na thyroid hormones, cyane cyane mu mezi 3 ya mbere y'inda.

Kwirinda imiti ikomeye: Imwe mu miti (nka isotretinoin ikoreshwa mu kuvura acne ikomeye) ikize kuri vitamin A, irabujijwe igihe batwite kuko ishobora guteza ibibazo mu mikurire y’umwana.

Kurya indyo yuzuye: Irimo intungamubiri nk’uko umuganga abiteganya, harimo vitamin A, ariko mu rugero ruciriritse.

Ultrasound ya kare: Kugira ngo bagaragaze niba hari ikibazo cy’imiterere (anatomical anomalies) hakiri kare.

Muri make:

Imisemburo ifasha umwana gukura neza munda. Iyo ikabije cyangwa ikabije kuba nke, ishobora gutera ibibazo bikomeye birimo no kuba umutima utakura neza mu gituza (ectopia cordis). Isuzuma ry’imisemburo, kwirinda imiti mibi, no kurya neza bifasha kugabanya ibyago.